N-Isovalerylglycine

本公司产品仅用于科研实验，不得用于人体或动物的临床与诊断

异戊酰甘氨酸 (IVG) 是一种酰基甘氨酸。酰基甘氨酸通常是脂肪酸的次要代谢物。然而，某些酰基甘氨酸的排泄在一些先天性代谢缺陷中会增加。在某些情况下，体液中这些代谢物的测量可用于诊断与线粒体脂肪酸β-氧化相关的疾病。

Isovalerylglycine (IVG) is an acyl glycine. Acyl glycines are normally minor metabolites of fatty acids. However the excretion of certain acyl glycines is increased in several inborn errors of metabolism. In certain cases the measurement of these metabolites in body fluids can be used to diagnose disorders associated with mitochondrial fatty acid beta-oxidation. Acyl glycines are produced through the action of glycine N-acyltransferase which is an enzyme that catalyzes the chemical reaction: acyl-CoA + glycine < -- > CoA + N-acylglycine. Isovalerylglycine is a byproduct of the catabolism of the amino acid leucine. Accumulation of isovalerylglycine occurs in Isovaleric Acidemia (IVA).

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N-Isovaleroylglycine | Isovaleroylglycine

Others

Other Targets

Others

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16284-60-9

159.18

C7H13NO3

>98% (HPLC)

DMSO: 5 mg/mL;Methanol: 2 mg/mL

CC(C)CC(=O)NCC(O)=O

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(-20℃)

With Ice Pack

≥ 2 years